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Surgical Management and Outcomes of Ebstein Anomaly in Neonates and Infants: A Society of Thoracic Surgeons Congenital Heart Surgery Database Analysis

This STS Database review included 255 neonates and 239 infants with Ebstein anomaly (EA). For neonates, repair was performed in 40%, shunt in 20%, and tricuspid valve closure in 9%; operative mortality was 27%. For infants, superior cavopulmonary anastomosis was performed in 38% and repair in 16%. Operative mortality was 9%. Optimal approach and timing for repair remain elusive.

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